Enzymes - Mock Test 36

Question 351

The enzyme deficient in Krabbe’s disease is?

A) Hexosaminidase A B) Arylsuphatase A C) β-Galactosidase D) α-Fucosidase

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Question 352

An important finding in Tay-sach’s disease is?

A) Renal failure B) Accumulation of gangliosides in brain and spleen C) Cardiac failure D) Anemia

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Question 353

The hypothesis to explain enzyme– substrate complex formation?

A) Lock and key model B) Induced fit theory C) Proenzyme theory D) Both 1⃣ and 2⃣

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Question 354

α-Galactosidase enzyme is defective in?

A) Tay-sach’s disease B) Refsum’s disease C) Sandhoff’s disease D) Fabry’s disease

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Question 355

An important finding in Refsum’s disease is?

A) Accumulation of ceramide trihexoside in the kidney B) Accumulation of phytanic acid in the blood and tissues C) Accumulation of gangliosides in brain and spleen D) Skin eruption

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Question 356

Refsum’s disease is due to deficiency of the enzyme?

A) Pytantate-α-oxidase B) Glucocerebrosidase C) Galactocerebrosidase D) Ceramide trihexosidase

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Question 357

The affected organ in Mc Ardle’s syndrome is?

A) Liver B) Kidney C) Liver and Heart D) Skeletal muscle

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Question 358

An important feature of Von-Gierke’s disease is?

A) Muscle cramps B) Cardiac failure C) Hypoglycemia D) Respiratory alkalosis

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Question 359

In Hunter’s syndrome?

A) There is progressive corneal opacity B) Keratan sulphate is excreted in the urine C) Enzyme defective is arylsulphatase B D) Hearing loss is perceptive

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Question 360

Defective enzyme in Hur’s syndrome is?

A) α-L-iduronidase B) Iduronate sulphatase C) Arylsulphatase B D) C-acetyl transferasente

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